Carglumic Acid
97%
- Product Code: 64889
CAS:
1188-38-1
Molecular Weight: | 190.15 g./mol | Molecular Formula: | C₆H₁₀N₂O₅ |
---|---|---|---|
EC Number: | MDL Number: | ||
Melting Point: | Boiling Point: | ||
Density: | Storage Condition: | -20℃ |
Product Description:
Carglumic acid is primarily used in the treatment of hyperammonemia, a condition characterized by elevated levels of ammonia in the blood. It is particularly effective in managing hyperammonemia caused by N-acetylglutamate synthase (NAGS) deficiency, a rare genetic disorder. By acting as a substitute for N-acetylglutamate, it helps activate the urea cycle, enabling the body to convert toxic ammonia into urea, which is then excreted through urine. This helps prevent the neurological damage and life-threatening complications associated with high ammonia levels. Additionally, it may be used in conjunction with other therapies for other urea cycle disorders to stabilize ammonia levels and improve patient outcomes.
Product Specification:
Test | Specification |
---|---|
APPEARANCE | White to off-white Solid |
PURITY | 96.5-100 |
Infrared spectrum | Conforms to Structure |
1 H NMR Spectrum | Consistent with structure |
Sizes / Availability / Pricing:
Size (g) | Availability | Price | Quantity |
---|---|---|---|
5.000 | 10-20 days | ฿1,660.00 |
+
-
|
25.000 | 10-20 days | ฿4,820.00 |
+
-
|
Carglumic Acid
Carglumic acid is primarily used in the treatment of hyperammonemia, a condition characterized by elevated levels of ammonia in the blood. It is particularly effective in managing hyperammonemia caused by N-acetylglutamate synthase (NAGS) deficiency, a rare genetic disorder. By acting as a substitute for N-acetylglutamate, it helps activate the urea cycle, enabling the body to convert toxic ammonia into urea, which is then excreted through urine. This helps prevent the neurological damage and life-threatening complications associated with high ammonia levels. Additionally, it may be used in conjunction with other therapies for other urea cycle disorders to stabilize ammonia levels and improve patient outcomes.
Mechanism | - |
Appearance | - |
Longevity | - |
Strength | - |
Storage | - |
Shelf Life | - |
Allergen(s) | - |
Dosage (Range) | - |
Recommended Dosage | - |
Dosage (Per Day) | - |
Recommended Dosage (Per Day) | - |
Mix Method | - |
Heat Resistance | - |
Stable in pH range | - |
Solubility | - |
Product Types | - |
INCI | - |
Cart
No products
Subtotal:
฿0.00
฿0.00
Total :