Butyrylcarnitine
98%
- Product Code: 110065
CAS:
25576-40-3
Molecular Weight: | 231.29 g./mol | Molecular Formula: | C₁₁H₂₁NO₄ |
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EC Number: | MDL Number: | ||
Melting Point: | Boiling Point: | ||
Density: | Storage Condition: | -20°C, airtight, dry |
Product Description:
Butyrylcarnitine is primarily used in medical diagnostics, particularly in screening for metabolic disorders. It serves as a biomarker for identifying conditions like short-chain acyl-CoA dehydrogenase deficiency (SCADD), a rare genetic disorder affecting fatty acid metabolism. Elevated levels of butyrylcarnitine in blood or urine samples can indicate metabolic imbalances, aiding in early detection and management of such conditions. Additionally, it is utilized in research studies to understand fatty acid oxidation processes and their role in energy production. This compound is also relevant in developing therapeutic strategies for metabolic diseases.
Product Specification:
Test | Specification |
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Appearance | White To Off-White Solid |
Purity (%) | 97.5-100 |
Infrared Spectrum | Conforms To Structure |
NMR | Conforms To Structure |
Sizes / Availability / Pricing:
Size (g) | Availability | Price | Quantity |
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0.005 | 10-20 days | $892.70 |
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Butyrylcarnitine
Butyrylcarnitine is primarily used in medical diagnostics, particularly in screening for metabolic disorders. It serves as a biomarker for identifying conditions like short-chain acyl-CoA dehydrogenase deficiency (SCADD), a rare genetic disorder affecting fatty acid metabolism. Elevated levels of butyrylcarnitine in blood or urine samples can indicate metabolic imbalances, aiding in early detection and management of such conditions. Additionally, it is utilized in research studies to understand fatty acid oxidation processes and their role in energy production. This compound is also relevant in developing therapeutic strategies for metabolic diseases.
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