3-Methylglutaconic Acid
98%
- Product Code: 209884
CAS:
5746-90-7
| Molecular Weight: | 144.13 g./mol | Molecular Formula: | C₆H₈O₄ |
|---|---|---|---|
| EC Number: | MDL Number: | MFCD01556044 | |
| Melting Point: | 101 - 105 °C (lit.) | Boiling Point: | 399.4 °C at 760 mmHg (lit.) |
| Density: | Storage Condition: | 2-8°C |
Product Description:
Used as a diagnostic biomarker in organic acidurias, particularly in mitochondrial disorders. Elevated levels in urine indicate impaired mitochondrial function and are associated with 3-methylglutaconic aciduria, a group of inherited metabolic diseases. Helps clinicians differentiate between subtypes of metabolic disorders when combined with clinical and genetic findings. Also used in research settings to study mitochondrial metabolism and energy production pathways.
Product Specification:
| Test | Specification |
|---|---|
| APPEARANCE | Off-white to grey powder |
| Purity (%) | 97.5-100 |
| Infrared Spectrum | Conforms to Structure |
| NMR | Conforms to Structure |
Sizes / Availability / Pricing:
| Size | Availability | Price | Quantity |
|---|---|---|---|
| 0.050 G | 10-20 days | ฿4,690.00 |
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| 0.250 G | 10-20 days | ฿12,100.00 |
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| 1.000 G | 10-20 days | ฿35,660.00 |
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3-Methylglutaconic Acid
Used as a diagnostic biomarker in organic acidurias, particularly in mitochondrial disorders. Elevated levels in urine indicate impaired mitochondrial function and are associated with 3-methylglutaconic aciduria, a group of inherited metabolic diseases. Helps clinicians differentiate between subtypes of metabolic disorders when combined with clinical and genetic findings. Also used in research settings to study mitochondrial metabolism and energy production pathways.
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