Carglumic Acid
10mM in DMSO
- Product Code: 157673
CAS:
1188-38-1
| Molecular Weight: | 190.15 g./mol | Molecular Formula: | C₆H₁₀N₂O₅ |
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| Density: | Storage Condition: | -20°C |
Product Description:
Used in the treatment of hyperammonemia, particularly in patients with N-acetylglutamate synthase (NAGS) deficiency. It acts as a substitute for N-acetylglutamate, which is a required activator of carbamoyl phosphate synthetase 1 (CPS1), a key enzyme in the urea cycle. By activating CPS1, it helps lower elevated blood ammonia levels. Also used off-label in other urea cycle disorders and acute hyperammonemic crises. Administered orally, it supports long-term management and acute intervention in both pediatric and adult patients.
Sizes / Availability / Pricing:
| Size | Availability | Price | Quantity |
|---|---|---|---|
| 1ml | 10-20 days | ฿1,850.00 |
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Carglumic Acid
Used in the treatment of hyperammonemia, particularly in patients with N-acetylglutamate synthase (NAGS) deficiency. It acts as a substitute for N-acetylglutamate, which is a required activator of carbamoyl phosphate synthetase 1 (CPS1), a key enzyme in the urea cycle. By activating CPS1, it helps lower elevated blood ammonia levels. Also used off-label in other urea cycle disorders and acute hyperammonemic crises. Administered orally, it supports long-term management and acute intervention in both pediatric and adult patients.
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