Used in the treatment of Friedreich’s ataxia, a rare genetic neurodegenerative disease. It works by activating the Nrf2 pathway, which helps reduce oxidative stress and inflammation in nerve cells. This can slow down the progression of neurological damage and improve mitochondrial function in affected individuals. Clinical studies have shown it may improve motor function and activities of daily living in patients. It is taken orally and is designed to target the underlying cellular dysfunction in the disease rather than just managing symptoms.